Imaging Science in Dentistry

Korean Academy of Oral and Maxillofacial Radiology (대한영상치의학회)
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Melanotic neuroectodermal tumor of infancy

유아성 흑백 신경외배엽성 종양

  • Song Haeng-Un (Department of Oral and Maxilofacial Radiology, School of Dentistry, and Institute of Oral Biol Science, Chonbuk National University) ;
  • Koh Kwang-Joon (Department of Oral and Maxilofacial Radiology, School of Dentistry, and Institute of Oral Biol Science, Chonbuk National University)
  • 송행은 (전북대학교 치과대학 구강악안면방사선학교실 및 구강생체과학연구소) ;
  • 고광준 (전북대학교 치과대학 구강악안면방사선학교실 및 구강생체과학연구소)
  • Published : 2002.09.01
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Abstract

The melanotic neuroectodermal tumor of infancy is a rare neoplasm arising in the first year of life. A 33-day-old female infant had an enlarged alveolar ridge on the right anterior maxilla. Intraoral examination revealed a nonulcerative swelling at the site. An intraoral radiograph showed an ill-defined radiolucency on the right anterior maxilla and displacement of primary incisors from their alveolar sockets. CT scans revealed an expansion of the surrounding bone and partial destruction of the anterior wall of the premaxilla. Histopathologic examination showed the cytoplasm of neuroblastic cells and eosinophilic, epithelioid cells frequently contained a dark brown granular pigment that stained positively to vimentin and HMB45, focally positive to NSE and cytokeratin. Four weeks after the operation, CT scans showed a rapidly growing soft tissue mass occupying right maxillary sinus encroaching to the orbit and nasal cavity. The final diagnosis was made as a malignant melanotic neuroectodermal tumor of infancy.

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