Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Pulmonary Epithelioid Hemangioendothelioma that Underwent Unusual Malignant Course

비전형적인 악성경과를 보인 폐 유상피성 혈관내피종 1례

  • Yoon, Hyoung-Kyu (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Kim, Tae-Yeon (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Jung, Jung-Im (Department of Radiology, The Catholic University of Korea, College of Medicine) ;
  • Lee, Kyo-Young (Department of Pathology, The Catholic University of Korea, College of Medicine) ;
  • Moon, Hwa-Sik (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Park, Sung-Hak (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Song, Jeong-Sup (Department of Internal Medicine, The Catholic University of Korea, College of Medicine)
  • 윤형규 (가톨릭대학교 의과대학 내과학교실) ;
  • 김태연 (가톨릭대학교 의과대학 내과학교실) ;
  • 정정임 (가톨릭대학교 의과대학 방사선과학교실) ;
  • 이교영 (가톨릭대학교 의과대학 병리학교실) ;
  • 문화식 (가톨릭대학교 의과대학 내과학교실) ;
  • 박성학 (가톨릭대학교 의과대학 내과학교실) ;
  • 송정섭 (가톨릭대학교 의과대학 내과학교실)
  • Published : 2001.11.30
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Abstract

Pulmonary epithelioid hemangioendothelioma (PEH), originally termed an intravacular bronchioloalveolar tumor, is a rare pulmonary neoplasm with a vascular origin and slow rate of malignancy. It affects various organs such as the liver, the central nervous system, lung, etc. Clinically, pulmonary epithelioid hemangioendothelioma has been considered to be a borderline malignancy, a generally indolent and nonaggressive tumor that displaces the pulmonary parenchyma over a number of years by slowly enlarging the tumor nodule. The clinical course of PEH is known to be usually benign. Here we report an unusual case of PEH that was highly malignant and was eventually fatal. The PEH was confirmed by microscopic analysis and immunohistochemical staining of CD31+(a membrane receptor and a sensitive and specific marker for vascular lesions) from an open lung biopsy specimen.

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