Journal of Korean Neurosurgical Society

The Korean Neurosurgical Society (대한신경외과학회)
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Multiple Hemangioblastomas on Cerebellum and Spinal Cord in a Patient of Von Hippel-Lindau Disease - A Case Report -

본 히펠 린다우병 환자에서 소뇌와 척수에 동시에 발생한 혈관아세포종 - 증례보고 -

  • Yoon, Chang Sik (Department of Neurosurgery, Inha University, College of Medicine) ;
  • Ha, Young Soo (Department of Neurosurgery, Inha University, College of Medicine) ;
  • Park, Chong Oon (Department of Neurosurgery, Inha University, College of Medicine) ;
  • Hyun, Dong Keun (Department of Neurosurgery, Inha University, College of Medicine)
  • 윤창식 (인하대학교 의과대학 인하병원 신경외과학교실) ;
  • 하영수 (인하대학교 의과대학 인하병원 신경외과학교실) ;
  • 박종운 (인하대학교 의과대학 인하병원 신경외과학교실) ;
  • 현동근 (인하대학교 의과대학 인하병원 신경외과학교실)
  • Received : 2000.05.30
  • Accepted : 2001.07.20
  • Published : 2001.08.28
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Abstract

Hemangioblastomas are rare benign tumor of the central nervous system that commonly occur in the posterior fossa around the 4th ventricle. In case of von Hippel-Lindau disease, hemangioblastomas involve multiple regions such as cerebellum, spinal cord and brainstem but, rarely show simultaneous involvement of cerebellum and spinal cord. We have experienced a case of multiple hemangioblastomas that were located at the cerebellum, cervical cord and conus medullaris and also had multiple lesions that a part of von Hippel-Lindau disease ; retinal angioma, syringomyelia, multiple cyst on kidney and pancreas, renal cell carcinoma on left kidney. Hemangioblastomas on cerebellum and spinal cord were removed totally, retinal angioma was treated with laser photocoagulation and renal cell carcinoma was also totally excised. The authors report a case of von Hippel-Lindau disease had multiple located hemangioblastomas on cerebellum, cervical cord and conus medullaris with review of literature.

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