A Case of Spinal Cord Compression Caused by Rhabdomyosarcoma of the Mediastinum Associated with Type I Neurofibromatosis(NF Type I) - Case Report -

제 I 형 신경섬유종증에 병발하였던 종격동내 횡문근육종에 의한 척수압박 1례 - 증례보고 -

  • Kim, Sei-Yoon (Department of Neurosurgery, Wonju College of Medicine, Yonsei University) ;
  • Whang, Kum (Department of Neurosurgery, Wonju College of Medicine, Yonsei University) ;
  • Hong, Soon-Ki (Department of Neurosurgery, Wonju College of Medicine, Yonsei University) ;
  • Pyen, Jhin-Soo (Department of Neurosurgery, Wonju College of Medicine, Yonsei University) ;
  • Hu, Chul (Department of Neurosurgery, Wonju College of Medicine, Yonsei University) ;
  • Kim, Hun-Joo (Department of Neurosurgery, Wonju College of Medicine, Yonsei University) ;
  • Han, Young-Pyo (Department of Neurosurgery, Wonju College of Medicine, Yonsei University) ;
  • Lee, Myoung-Sup (Department of Diagnostic Radiology, Wonju College of Medicine, Yonsei University) ;
  • Lee, Chong-Kook (Department of Cardiothoracic Surgery, Wonju College of Medicine, Yonsei University) ;
  • Cho, Mee-Yon (Department of Pathology, Wonju College of Medicine, Yonsei University)
  • 김세윤 (연세대학교 원주의과대학 신경외과학교실) ;
  • 황금 (연세대학교 원주의과대학 신경외과학교실) ;
  • 홍순기 (연세대학교 원주의과대학 신경외과학교실) ;
  • 변진수 (연세대학교 원주의과대학 신경외과학교실) ;
  • 허철 (연세대학교 원주의과대학 신경외과학교실) ;
  • 김헌주 (연세대학교 원주의과대학 신경외과학교실) ;
  • 한용표 (연세대학교 원주의과대학 신경외과학교실) ;
  • 이명섭 (연세대학교 원주의과대학 진단방사선과학교실) ;
  • 이종국 (연세대학교 원주의과대학 흉부외과학교실) ;
  • 조미연 (연세대학교 원주의과대학 병리학교실)
  • Received : 2000.07.18
  • Accepted : 2001.04.10
  • Published : 2001.05.28

Abstract

A 12-years-old female admitted to the hospital with the complaint of pain on the right upper chest area which persisted about 1 month prior to admission. $Caf{\acute{e}}$-au-lait spots of various size laying on a whole body and freckling on the axilla were found on physical examination. A huge mass was found on the plain chest X-ray and on chest MRI. The mass encroached thoracic spine, posterior rib, back muscles, and then into the neural canal and compressed thoracic spinal cord. On the 5th day of hospitalization, the patient complained tingling on the both legs and 2 days later, monoparesis on the right leg. Open thoracotomy and decompressive laminectomy was done to remove mass. Pathologic reports confirmed rhabdomyosarcoma, embryonal type.

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