Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Pulmonary Cavernous Hemangiomatosis Presented with Right Shoulder Pain

우측 어깨의 통증을 주소로 내원한 해면상 폐혈관종증 1례

  • Lee, Eun-Young (Division of Pulmonary and Critical Medicine, Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Hong, Sang-Bum (Division of Pulmonary and Critical Medicine, Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Shim, Tae-Sun (Division of Pulmonary and Critical Medicine, Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Lim, Chae-Man (Division of Pulmonary and Critical Medicine, Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Koh, Youn-Suck (Division of Pulmonary and Critical Medicine, Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Woo-Sung (Division of Pulmonary and Critical Medicine, Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Dong-Soon (Division of Pulmonary and Critical Medicine, Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Won-Dong (Division of Pulmonary and Critical Medicine, Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Dong-Kwan (Division of Pulmonary and Critical Medicine, Department of Thoracic Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Lee, In-Chul (Division of Pulmonary and Critical Medicine, Department of Diagnostic Pathology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Moon, Dae-Hyuck (Division of Pulmonary and Critical Medicine, Department of Nuclear Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Lee, Sang-Do (Division of Pulmonary and Critical Medicine, Department of Internal Medicine, Asan Medical Center, University of Ulsan College of Medicine)
  • 이은영 (울산대학교 의과대학 서울중앙병원 내과학 교실) ;
  • 홍상범 (울산대학교 의과대학 서울중앙병원 내과학 교실) ;
  • 심태선 (울산대학교 의과대학 서울중앙병원 내과학 교실) ;
  • 임채만 (울산대학교 의과대학 서울중앙병원 내과학 교실) ;
  • 고윤석 (울산대학교 의과대학 서울중앙병원 내과학 교실) ;
  • 김우성 (울산대학교 의과대학 서울중앙병원 내과학 교실) ;
  • 김동순 (울산대학교 의과대학 서울중앙병원 내과학 교실) ;
  • 김원동 (울산대학교 의과대학 서울중앙병원 내과학 교실) ;
  • 김동관 (울산대학교 의과대학 서울중앙병원 흉부외과학 교실) ;
  • 이인철 (울산대학교 의과대학 서울중앙병원 진단병리학교실) ;
  • 문대혁 (울산대학교 의과대학 서울중앙병원 핵의학교실) ;
  • 이상도 (울산대학교 의과대학 서울중앙병원 내과학 교실)
  • Published : 2000.07.30
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Abstract

Pulmonary hemangiomatosis is a rare disease of unknown etiology characterized by diffuse proliferating microvessels that infiltrate not only the lung but also all of the thoracic tissues. The disease is rapidly progressive and usually results in death due to complications of pulmonary hypertension and pulmonary hemorrhage. There are two histologic patterns of pulmonary hemangiomatosis : capillary and cavernous. We describe a 21-year-old man with cavernous-type pulmonary hemangiomatosis presented with right side shoulder pain. He was treated with percutaneous transarterial embolization and then followed with interferon alfa-2a for one year with favorable clinical and radiological response.

폐혈관종증은 그 원인이 알려지지 않은 매우 드문 질환으로 폐와 그 주위 조직을 침범하는 미세혈관들의 증식을 특징으로 한다. 조직학적으로는 모세혈관 혈관종증과 해면상 혈관종증으로 나뉘는데, 많은 환자들이 보고되었다. 저자들은 우측어깨의 통증을 주소로 내원한 21세 남자 환자에서 해면상 폐혈관종증을 진단하고 1년간의 interferon alfa-2a치료를 시행하여 임상적, 방사선학적 호전을 경험하였다.

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