Advances in pediatric surgery

Korean Association of Pediatric Surgeons (대한소아외과학회)
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Two Cases of Pancreatoblastoma

췌모세포종 2예

  • Huh, Young-Soo (Division of Pediatric Surgery, Department of Surgery, College of Medicine, Yeungnam University) ;
  • Hah, Jeong-Ok (Department of Pediatrics, College of Medicine, Yeungnam University) ;
  • Jang, Seon-Mo (Division of Pediatric Surgery, Department of Surgery, College of Medicine, Yeungnam University) ;
  • Lee, Jung-Hoon (Division of Pediatric Surgery, Department of Surgery, College of Medicine, Yeungnam University)
  • 허영수 (영남대학교 의과대학 외과학교실 소아외과) ;
  • 하정옥 (영남대학교 의과대학 소아과학교실) ;
  • 장선모 (영남대학교 의과대학 외과학교실 소아외과) ;
  • 이정훈 (영남대학교 의과대학 외과학교실 소아외과)
  • Published : 2000.12.30
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Abstract

Pancreatoblastoma is uncommon in children and is exceedingly rare in adults. Prognosis is good if the tumor is removed prior to metastasis. Complete tumor resection is the most important factor for long survival. We report two cases of pancreatoblastoma in 4 and 7 years old girls. Palpable abdominal mass was accidentally found by their parents. Abdominal CT scan showed a huge retroperitoneal mass of unknown origin in one case and a mass involving the pancreas in the other case. At laparotomy, well encapsulated tumor mass($10{\times}10$ cm in maximum dimension) was noted in the body of pancreas in one case, and in the tail of pancreas in the other case( $8{\times}7$ cm). We resected the tumor and preserved the spleen in both cases. Histological examination revealed that the tumors were pancreatoblastoma. Patients received postoperative chemotherapy with 6 cycles of cisplatinum, adriamycin, ifosfamide and etoposide and are alive in good condition 19 months and 17 months after operation.

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