Left Thoracic Sympathetic Ganglionectomy with Thoracoscope for the Treatment of the Long QT Syndrome -A case report-

Long QT 증후군 환자에게 시행한 좌측 흉부 교감신경절 절제술 -1례 보고-

  • 홍남기 (영남대학교 의과대학 흉부외과학 교실) ;
  • 정태은 (영남대학교 의과대학 흉부외과학 교실) ;
  • 이정철 (영남대학교 의과대학 흉부외과학 교실) ;
  • 한승세 (영남대학교 의과대학 흉부외과학 교실) ;
  • 이동협 (영남대학교 의과대학 흉부외과학 교실)
  • Published : 2000.09.01

Abstract

The long QT syndromes have been classified into acquired or inheritary forms, both of which are associated with a characteristic type of life-threatening polymorphic ventricular tachycardia called torsade de points. Beta-adrenergic blocker is the first cholic treatment, but in those whom cardiac events are not prevented by $\beta$-blockade, left thoracic sympathetic ganglionectomy may be useful in selected cases. A 50-year-old woman had an recurrent syncopal attack in which she was unconscious for 1-2 min and 1-2 times a month for 10 years. The EKG revealed that QT & QTc intervals were 744 and 632 msec respectively. Treatment with Beta-adrenergic blocker and calcium channel blocker was ineffective in preventing recurrence of syncopal spell. Therefore, she underwent left thoracic sympathetic ganglionectomy with thoracoscope. During the 9 months after operation, she was free of syncopal episodes and is doing well.

Keywords

References

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