Childhood Kidney Diseases
- Volume 3 Issue 2
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- Pages.221-226
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- 1999
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- 2384-0242(pISSN)
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- 2384-0250(eISSN)
A Case Report Unilaterally Involved Glomerulocystic Kidney Disease
단측에 발생한 사구체낭성신질환 1례
- Oh Seung-Jin (Departments of Pediatrics, and The Institute of Kidney Disease, Yonsei University College of Medicine) ;
- Yook Jin-Won (Departments of Pediatrics, and The Institute of Kidney Disease, Yonsei University College of Medicine) ;
- Kim Ji-Hong (Departments of Pediatrics, and The Institute of Kidney Disease, Yonsei University College of Medicine) ;
- Chung Hyun-Ju (Departments of Pathology, and The Institute of Kidney Disease, Yonsei University College of Medicine) ;
-
Kim Myung-Joon
(Departments of Radiology, and The Institute of Kidney Disease, Yonsei University College of Medicine)
;
- Kim Pyung-Kil (Departments of Pediatrics, and The Institute of Kidney Disease, Yonsei University College of Medicine)
- 오승진 (연세대학교 의과대학 소아과학교실 및 신장질환연구소) ;
- 육진원 (연세대학교 의과대학 소아과학교실 및 신장질환연구소) ;
- 김지홍 (연세대학교 의과대학 소아과학교실 및 신장질환연구소) ;
- 정현주 (연세대학교 의과대학 병리학교실 및 신장질환연구소) ;
-
김명준
(연세대학교 의과대학 진단 방사선과학교실 및 신장질환연구소)
;
- 김병길 (연세대학교 의과대학 소아과학교실 및 신장질환연구소)
- Published : 1999.10.01
Abstract
Glomerulocystic kidney disease(GCKD) is a rare form of renal cystic disease defined histopathologically by containing dilated Bowman's space with variable atrophy of glomerular tufts, which may occur as sporadically or as familial cases and can be presented as a major component of heritable syndromes. It has not been recognized in Korean children but only one report of adult case has been reported having GCKD. We experienced a case of GCKD in a 10-year-10-month-old boy, who was admitted for hypertension. Abdominal ultrasonography and computed tomography revealed clustered numerous small cysts in left kidney and renal biopsy findings was consistent with the GCKD showing cystic dilatation of Bowman's space with intact glomerular structure.