Advances in pediatric surgery
- Volume 5 Issue 2
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- Pages.137-140
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- 1999
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- 2635-8778(pISSN)
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- 2635-8786(eISSN)
Splenic Rupture in Congenital Afibrinogenemia
선천성 무섬유소원혈증 환자에 발생한 비장 파열의 치료
- Kim, Dae-Yeon (Department of Surgery, Ulsan University College of Medicine) ;
- Kim, Seong-Chul (Department of Surgery, Ulsan University College of Medicine) ;
- Kim, In-Koo (Department of Surgery, Ulsan University College of Medicine)
- Published : 1999.12.30
Abstract
Congenital afibrinogenemia is a rare disorder characterized by a congenital lack of fibrinogen, a key component of the hemostatic system. Bleeding manifestations of congenital afibrinogenemia vary in severity from mild to catastrophic. This is a case report of splenic rupture occurred in an eight-year-old boy with congenital afibrinogenemia. Nonoperative treatment with cryoprecipitate and virally inactivated, purified fibrinogen concentrates successfully avoided splenectomy.