Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Pulmonary Lymphangioleiomyomatosis with Pneumothorax

기흉을 합병한 폐림프관평활근종증 치험 1례

  • 장인성 (순천향대학교 천안병원 흉부외과) ;
  • 이준복 (순천향대학교 천안병원 흉부외과) ;
  • 고정관 (순천향대학교 천안병원 흉부외과) ;
  • 양성린 (순천향대학교 천안병원 흉부외과) ;
  • 김용훈 (순천향대학교 천안병원 호흡기내과) ;
  • 이철세 (순천향대학교 천안병원 흉부외과)
  • Published : 1999.11.01
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Abstract

Lymphangioleiomyomatosis(LAM) is defined as an abnormal proliferation of smooth muscles in the lung tissue throughout lymphatics, vascular and bronchial structure. A 52-year-old postmenopausal woman was admitted to our hospital for recurrent pneumothorax. She was treated for medroxyprogesterone by LAM 1 month ago. We performed operation of pulmonary partial resection and pleurodesis. The patient is receiving continuous medroxyprogesterone and Leuplin administration, and currently, 6 months after the operation, is still showing good results.

Keywords

References

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