A Case of Asphyxiating Thoracic Dystrophy with Chronic Renal Failure

만성 신부전이 동반된 Asphyxiating Thoracic Dystrophy 1례

  • Cho Hyun-Jung (Department of Pediatrics, Catholic University, Medical College) ;
  • Lee Yoon-Kyung (Department of Pediatrics, Catholic University, Medical College) ;
  • Kim Dong-Un (Department of Pediatrics, Catholic University, Medical College) ;
  • Lee Ik-Jun (Department of Pediatrics, Catholic University, Medical College)
  • 조현정 (가톨릭대학교 의과대학 소아과학교실) ;
  • 이윤경 (가톨릭대학교 의과대학 소아과학교실) ;
  • 김동언 (가톨릭대학교 의과대학 소아과학교실) ;
  • 이익준 (가톨릭대학교 의과대학 소아과학교실)
  • Published : 1998.08.01

Abstract

The classical manifestation of asphyxiating thoracic dystrophy comprise narrow chest, short limbs, and pelvic changes. The degree of respiratory distress varied from negligible to lethal. The development of progressive renal failure may indicate that the condition is asphyxiating thoracic dystrophy. We have experienced a case of asphyxiating thoracic dystrophy who died from chronic renal failure in a 5-month old infant. Abriefreviewofassociatedliteratureisalsopresented.

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