Peutz-Jeghers Syndrome in Korean

한국 Peutz-Jeghers 증후군의 특징

  • Lee, Seong-Cheol (Department of Pediatric Surgery, Seoul National University Children's Hospital) ;
  • Lee, Hyeon-Kook (Department of Pediatric Surgery, Seoul National University Children's Hospital) ;
  • Yang, Suk-Jin (Department of Pediatric Surgery, Seoul National University Children's Hospital) ;
  • Jung, Sung-Eun (Department of Pediatric Surgery, Seoul National University Children's Hospital) ;
  • Park, Kwi-Won (Department of Pediatric Surgery, Seoul National University Children's Hospital) ;
  • Kim, Woo-Ki (Department of Pediatric Surgery, Seoul National University Children's Hospital)
  • 이성철 (서울대학교 어린이병원 소아외과) ;
  • 이현국 (서울대학교 어린이병원 소아외과) ;
  • 양석진 (서울대학교 어린이병원 소아외과) ;
  • 정성은 (서울대학교 어린이병원 소아외과) ;
  • 박귀원 (서울대학교 어린이병원 소아외과) ;
  • 김우기 (서울대학교 어린이병원 소아외과)
  • Published : 1997.06.30

Abstract

Eight pediatric patients with Peutz-Jeghers syndrome were treated from 1984 to 1994 at the Department of Surgery, Seoul National University Children's Hospital. We reviewed the clinical features of our own 8 cases as well as 56 cases reported in Korean literatures. The results were compared to those of western reports. Gastrointestinal complications in our series were more frequent than in the Korean series, but the distribution of polyps was similar. The Korean series showed the following characteristics compared to the western reports; demographic backgrounds were similar; gastrointestinal symptoms were more common; location of the polyp was more frequent in colon (2 times); and the most prevalent site of malignant change was the colon in Korean cases.

Keywords

Acknowledgement

Supported by : 서울대학교병원