굴곡성 기관지경하 전기소각술로 치료한 미만성 기관기관지형 유전분증 1예

Treatment of Diffuse Tracheobronchial Amyloidosis by Repeated Electrocautry Under Fiberoptic Bronchoscopy

  • 김호중 (한림대학교 의과대학 내과학교실) ;
  • 고종훈 (한림대학교 의과대학 내과학교실) ;
  • 장명준 (한림대학교 의과대학 내과학교실) ;
  • 홍성훈 (한림대학교 의과대학 내과학교실) ;
  • 김경환 (한림대학교 의과대학 내과학교실) ;
  • 현인규 (한림대학교 의과대학 내과학교실) ;
  • 이명구 (한림대학교 의과대학 내과학교실) ;
  • 정기석 (한림대학교 의과대학 내과학교실)
  • Kim, Ho-Joong (Department of Internal Midicine, Hallym University College of Medicine) ;
  • Koh, Jong-Hoon (Department of Internal Midicine, Hallym University College of Medicine) ;
  • Chang, Myeong-Jun (Department of Internal Midicine, Hallym University College of Medicine) ;
  • Hong, Sung-Hun (Department of Internal Midicine, Hallym University College of Medicine) ;
  • Kim, Kyung-Hwan (Department of Internal Midicine, Hallym University College of Medicine) ;
  • Hyun, In-Kyu (Department of Internal Midicine, Hallym University College of Medicine) ;
  • Lee, Myoung-Koo (Department of Internal Midicine, Hallym University College of Medicine) ;
  • Jung, Ki-Suck (Department of Internal Midicine, Hallym University College of Medicine)
  • 발행 : 1995.04.30

초록

미만성 기관기관지형 유전분증은 폐를 침범하는 유전분증 중에서 기침, 호흡곤란, 혈담 및 반복되는 폐렴 등의 증상을 일으키고 기관지경 검사에서 기관 및 여러 기관지에 종괴를 형성하는 질환이다. 저자들은 58세 여자 환자에서 발생한 미만성 기관기관지형 유전분증을 기관지경하 생검으로 진단하고 전기조작술을 시행하여 기관지협착을 성공적으로 치료한 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Diffuse tracheobronchial amyloidosis is an uncommon form of pulmonary involvement, and causes prolonged cough, dyspnea, wheezing and repeated development of pneumonia. We report a case of diffuse tracheobronchial amyloidosis in 58-year-old woman that was traeted by repeated electrocautry under flexible fiberoptic bronchoscopy. The patient had a long-standing history of dyspnea and was admitted due to resting dyspnea, which was aggravated to impending respiratory failure after diagnostic procedures. We applied repeated electrocautry to the endobronchial amyloid tumors and successfully reduced bronchial stenosis and the pateint didn't feel dyspnea. We suppose that, in certain cases of tracheobronchial amyloidosis patients, endobronchial electrocautry would be a helpful procedure.

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