Hirschsprung's Disease Associated with Neonatal Intestinal Perforation

장 천공을 동반한 Hirschsprung씨 병 3예 보고

  • Kim, Seong-Chul (Department of Surgery, University of Ulsan College of Medicine, and Asan Medical Center) ;
  • Sea, Byong-Sun (Department of Surgery, University of Ulsan College of Medicine, and Asan Medical Center) ;
  • Liu, Shan King (Department of Surgery, University of Ulsan College of Medicine, and Asan Medical Center) ;
  • Kim, In-Koo (Department of Surgery, University of Ulsan College of Medicine, and Asan Medical Center)
  • 김성철 (울산대학교 의과대학 외과학교실) ;
  • 서병선 (울산대학교 의과대학 외과학교실) ;
  • 유선경 (울산대학교 의과대학 외과학교실) ;
  • 김인구 (울산대학교 의과대학 외과학교실)
  • Published : 1995.11.15

Abstract

Neonatal intestinal perforation is mainly caused by necrotizing enterocolitis, intestinal atresia, meconium ileus or unknown etiology. Occasionally, Hirschsprung's disease presents with neonatal intestinal perforation, of which, it is known that total colonic aganglionosis is common. Therefore, Hirschsprung's disease should be considered as a cause of neonatal intestinal perforation. The authors have experienced 3 cases of neonatal Hirschsprung's disease associated with colonic perforations. Cecal perforations were noted in 2 cases with aganglionosis from descending colon and sigmoid perforation in a case with aganglionosis in rectum. These cases will be discussed with literature review.

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