Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Surgical Treatment of Supravalvular Aortic Stenosis

대동맥 판상부 협착증의 수술요법

  • 유재현 (부천 세종병원 흉부외과, 세종의학연구소) ;
  • 유환국 (부천 세종병원 흉부외과, 세종의학연구소) ;
  • 이원용 (부천 세종병원 흉부외과, 세종의학연구소) ;
  • 나찬영 (부천 세종병원 흉부외과, 세종의학연구소) ;
  • 정윤섭 (부천 세종병원 흉부외과, 세종의학연구소) ;
  • 김응수 (부천 세종병원 흉부외과, 세종의학연구소) ;
  • 백완기 (부천 세종병원 흉부외과, 세종의학연구소) ;
  • 한재진 (부천 세종병원 흉부외과, 세종의학연구소) ;
  • 이영탁 (부천 세종병원 흉부외과, 세종의학연구소)
  • Published : 1993.02.01
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Abstract

Supravalvular aortic stenosis is an uncommon, congenital narrowing of ascending aorta just above aortic valve. Eleven patients underwent an aortoplasty to relieve supravalvular aortic stenosis at Sejong General Hospital from July 1985 to December 1991. Age ranged from 5 to 14 years(median 9 years). There were 7 male and 4 female patients. Seven patients had characteristics of Williams' syndrome including elfin face and mental retardation. All patients had localized, hourglass type but 4 patients had atypical findings. Preoperative left ventricula-aortic pressure gradient ranged from 40 to 190 mmHg(mean 88 mmHg). To relieve severe supravalvular aortic stenosis, extended aortoplasty was used in 7 patients and standard aortoplasty in 4 patients. Postoperative pressure gradient ranged from 0 to 40 mmHg (mean 16.6 mmHg). Follow-up pressure gradient with Doppler ranged from 0 to 88mmHg(mean 32.5mmHg).

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