Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Pulmonary Lymphangioleiomyomatosis

폐의 임파관 평활근종증 1예

  • Kang, Sung-Yi (Department of Internal Medicine, College of Medicine, Kyung Hee University) ;
  • Yoon, Ki-Heon (Department of Internal Medicine, College of Medicine, Kyung Hee University) ;
  • Yoo, Jee-Hong (Department of Internal Medicine, College of Medicine, Kyung Hee University) ;
  • Kang, Hong-Mo (Department of Internal Medicine, College of Medicine, Kyung Hee University) ;
  • Yang, Moon-Ho (Department of Pathology, College of Medicine, Kyung Hee University)
  • 강성이 (경희대학교 의과대학 내과학교실) ;
  • 윤기헌 (경희대학교 의과대학 내과학교실) ;
  • 유지홍 (경희대학교 의과대학 내과학교실) ;
  • 강흥모 (경희대학교 의과대학 내과학교실) ;
  • 양문호 (경희대학교 의과대학 병리학교실)
  • Published : 1992.06.30
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Abstract

Pulmonary lymphangioleiomyomatosis is a rare disease, prevalent in women of reproductive age, and characterized by proliferation of atypical smooth muscle in the lung. A 44-year-old women with pulmonary lymphangioleiomyomatosis was presented. Chest radiographs showed diffuse increased reticulonoular infiltrations on the almost entire lung and high resolution CT illustrated multiple, well defined cystic lesions which were distributed diffusely through the lung. Histologic confirmation of lymphangioleiomyomatosis was made upon open lung biopsy. Treatment with methylprogesterone was initated.

저자들은 운동시 호흡곤란을 주소로 내원한 44세 여자환자에서 개흉 폐생검을 통해 확진한 폐의 임파관 평활근종증 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

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