Maxillofacial Plastic and Reconstructive Surgery

Korean Association of Maxillofacial Plastic and Reconstructive Surgeons (대한악안면성형재건외과학회)
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STURGE-WEBER SYNDROME;REPORT OF THREE CASES

STURGE-WEBER 증후군의 문헌고찰과 증례보고

  • Rim, Jae-Suk (Dept. of Dentistry, Guro Hospital, College of Medicine, Korea University) ;
  • Kim, Sung-Moon (Dept. of Dentistry, Guro Hospital, College of Medicine, Korea University) ;
  • Kim, Onn (Dept. of Dentistry, Guro Hospital, College of Medicine, Korea University) ;
  • Ryu, Jae-Jun (Dept. of Dentistry, Guro Hospital, College of Medicine, Korea University)
  • Published : 1989.12.31
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Abstract

Sturge - Weber Syndrome is a congenital disorder and characterized by facial hemangioma following one or more divisions of the trigeminal nerve, epilepsy, mental retardation, contralateral hemiplegia, occlular involvement, gingival involvement. A 34 year old Korean man, a 25 year old Korean woman and a 48 year old Korean woman were found to have red - purple colored pigmentation on the hemifacial area and upper oral mucosal area.

Sturge-Weber syndrome은 드물게 볼 수 있는 선천성질환으로 일명 encephalotrigeminal angiomatosis, 또는 Sturge-Weber-Dimitri syndrome이라 하며 삼차신경의 분지를 따라 분포하는 안면 혈관종, 안면 혈관종과 같은 부위의 intracerebral calcification, 경련의 특징을 가진다. 이에 저자들은 Sturge-Weber syndrome 3예를 치험하였기에 문헌고찰과 함께 보고하는 바이다.

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