Journal of Yeungnam Medical Science
- Volume 2 Issue 1
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- Pages.259-264
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- 1985
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- 2799-8010(eISSN)
A Case of Neuroblastoma Presenting with Sudden Blindness
실명을 주소로 한 신경아세포종 1예
- Ma, In-Youl (Department of Pediatrics College of Medicine, Yeungnam University) ;
- Hah, Jeong-Ok (Department of Pediatrics College of Medicine, Yeungnam University) ;
- Kim, Chun-Dong (Department of Pediatrics College of Medicine, Yeungnam University) ;
- Lee, Tae-Sook (Department of Pathology College of Medicine, Yeungnam University)
- Published : 1985.06.30
Abstract
Neuroblastoma is the most common extracranial solid tumor of childhood which presents various clinical symptoms depending on the primary and metastatic sites. However, it has been rarely reported that sudden onset of blindness was the chief complaint of neuroblastoma. A four years old boy was admitted to the Yeungnam University Hospital with the chief complaint of a sudden onset of blindness due to a distant metastasis of abdominal neuroblastoma to the sphenoid sinus. On admission, both side pupils were dilated without light reflex, fundoscopy showed pale optic disk, electroretinogram was subnormal and visual evoked potential showed no response. The liver was palpable in
신경아세포종은 소아기에 발생하는 악성종양중 뇌종양 다음으로 흔히 발생하는 것으로 원발 혹은 전이된 부위에 따라 다양한 임상증상이 나타날 수 있으나 실명을 주소로 한 경우는 드물다. 본 증례는 4세된 남아의 복부에서 기원하여 사골동으로 원위전이하여 갑작스런 실명을 주소로 한 신경아세포종으로 cytoxan, vincristine, DTIC, adriamycin 및 VM-26의 병합요법으로 치료하여 실명은 그대로 있으나 복부와 사골동의 종괴는 현저히 감소하였고 환아는 건강이 양호한 상태이다.
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